Gravholt, Claus H;
Andersen, Niels H;
Christin-Maitre, Sophie;
Davis, Shanlee M;
Duijnhouwer, Anthonie;
Gawlik, Aneta;
Maciel-Guerra, Andrea T;
Gutmark-Little, Iris;
Fleischer, Kathrin;
Hong, David;
Klein, Karen O;
Prakash, Siddharth K;
Kanakatti Shankar, Roopa;
Sandberg, David E;
Sas, Theo C. J;
Skakkebæk, Anne;
Stochholm, Kirstine;
van der Velden, Janielle A.
Turner syndrome (TS) affects 50 per 100 000 females. TS affects multiple organs through all stages of life, necessitating multidisciplinary care. This guideline extends previous ones and includes important new advances, within diagnostics and genetics, estrogen treatment, fertility, co-morbidities, and n...
Fassnacht, M;
Dekkers, OM;
Else, T;
Baudin, E;
Berruti, A;
de Krijger, R;
Haak, HR;
Mihai, R;
Assie, G;
Terzolo, M.
Adrenocortical carcinoma (ACC) is a rare and in most cases steroid hormone-producing tumor with variable prognosis. The purpose of these guidelines is to provide clinicians with best possible evidence-based recommendations for clinical management of patients with ACC based on the GRADE (Grading of Recomm...
Neoplasias de la Corteza Suprarrenal,
Metástasis de la Neoplasia,
Antineoplásicos Hormonales/uso terapéutico,
Etopósido/administración & dosificación,
Mitotano/uso terapéutico,
Doxorrubicina/uso terapéutico,
Carcinoma Corticosuprarrenal/diagnóstico,
Carcinoma Corticosuprarrenal,
Carcinoma Corticosuprarrenal/tratamiento farmacológico,
Radioterapia,
Cisplatino/uso terapéutico,
Protocolos de Quimioterapia Combinada Antineoplásica/uso terapéutico,
Ablación por Catéter,
Adrenalectomía,
Neoplasias de la Corteza Suprarrenal/terapia,
Carcinoma Corticosuprarrenal/terapia,
Quimioembolización Terapéutica
BACKGROUND: Pituitary tumours are common and easily treated by surgery or medical treatment in most cases. However, a small subset of pituitary tumours does not respond to standard medical treatment and presents with multiple local recurrences (aggressive pituitary tumours) and in rare occasion with meta...
Fassnacht, M;
Arlt, W;
Bancos, I;
Dralle, H;
Newell-Price, J;
Sahdev, A;
Tabarin, A;
Terzolo, M;
Tsagarakis, S;
Dekkers, OM.
By definition, an adrenal incidentaloma is an asymptomatic adrenal mass detected on imaging not performed for suspected adrenal disease. In most cases, adrenal incidentalomas are nonfunctioning adrenocortical adenomas, but may also represent conditions requiring therapeutic intervention (e.g. adrenocorti...
Hypoparathyroidism (HypoPT) is a rare (orphan) endocrine disease with low calcium and inappropriately low (insufficient) circulating parathyroid hormone levels, most often in adults secondary to thyroid surgery. Standard treatment is activated vitamin D analogues and calcium supplementation and not repla...